Rathke Cleft Cyst in Seven Year-old Girl Presenting with Central Diabetes Insipidus and Review of Literature
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Olcay Evliyaoglu
ABSTRACT
Rathke cleft cysts (RCC) are benign cysts derived from remnants of Rathke cleft, and are rarely symptomatic in children. Symptoms due to RCC are associated with mass effect and pituitary hormone deficiencies. Slow growth rate of the cyst makes its incidence increase with aging. Here we report on a seven year old girl who presented with central diabetes insipidus (CDI). Her sella MRI revealed a lesion in the sellar region which grew rapidly in follow-up. She underwent microneurosurgical operation and the lesion was totally excised. Pathologic examination revealed RCC with degenerative changes. In her follow-up, growth hormone deficiency developed in addition to arginine vasopressin deficiency. Rapid growth of the cyst is not the usual course of RCC's. Mechanisms regarding the cyst growth are unclear as they are in this case. This is the youngest child to date presenting with central diabetes insipidus due to RCC. Rapid growth of RCC can cause CDI in young children.
© Freund Publishing House Ltd. 2010
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- Rathke Cleft Cyst in Seven Year-old Girl Presenting with Central Diabetes Insipidus and Review of Literature
Artikel in diesem Heft
- The Functional Food Era
- Pituitary Adenomas in Children and Adolescents
- Hypothalamic Hamartoma Causing Precocious Puberty in a Female Child
- “Functional Food” for Acceleration of Growth in Short Children Born Small for Gestational Age
- Cognition, Emotions and Quality of Life in Lithuanian Girls with Turner Syndrome after Growth Hormone Therapy Discontinuation
- Predictors and Growth Consequences of Central Hypothyroidism in Pediatric Patients Receiving Recombinant Human Growth Hormone
- Serum Levels of Adiponectin and Leptin in Children Born Small for Gestational Age: Relation to Insulin Sensitivity Parameters
- Growth Hormone Response to GH-Releasing Peptide-2 in Children
- The Evaluation of the Adrenal and Thyroid Axes and Glucose Metabolism after Burn Injury in Children
- The Relationship between Vitamin D Receptor Gene Polymorphisms and Bone Density, Osteocalcin Level and Growth in Adolescents
- Elevated Plasma Levels of Apelin in Children with Type 1 Diabetes Mellitus
- Chronic Intermittent Form of Isovaleric Acidemia Mimicking Diabetic Ketoacidosis
- Obesity and Reversed Growth Retardation in a Child with Type Ia Glycogen Storage Disease
- Another Unusual Presentation of McCune Albright Syndrome with Fibrous Dysplasia, Unilateral Testicular Enlargement, and Testicular Microlithiasis
- Cystic Changes in the Ovaries of a Pre-pubertal Girl with Henoch-Schönlein Purpura
- A Case Report of Neonatal Diabetes Due to Neonatal Hemochromatosis
- Rathke Cleft Cyst in Seven Year-old Girl Presenting with Central Diabetes Insipidus and Review of Literature
