Prenatal diagnosis of right aortic arch: associated anomalies and fetal prognosis according to different subtypes
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Gizem Elif Dizdaroğulları
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Abdullah Alpınar
Abstract
Objectives
Right aortic arch (RAA) is a rare anomaly with an incidence of 0.1 % in the adult population and low-risk fetuses. Our aim in this study was to evaluate associated anomalies and conditions according to subtypes.
Methods
This was a retrospective study examining consecutive pregnancies diagnosed with RAA in our hospital between 2018 and 2022. Fetuses with RAA were divided into three groups, RAA with right-sided ductus arteriosus (RAA-RDA), RAA with left-sided ductus arteriosus (RAA-LDA), and RAA with a double aortic arch (RAA-DAA).
Results
A total of 81 fetuses were diagnosed as having RAA during the study period. The rate of cardiac anomalies (82.8 %) in the RAA-RDA group was higher than in the RAA-LDA (17.6 %) and RAA-DAA (22.2 %) groups (p<0.001). No statistically significant difference was found between the groups in terms of maternal age, diagnosis week, pregnancy outcome, extracardiac anomalies, and genetic anomalies. Three (8 %) of 36 fetuses with isolated RAA who resulted in live birth developed symptoms related to the vascular ring, and one (2.7 %) newborn with RAA-DAA underwent surgery.
Conclusions
The incidence of cardiac anomalies is high in fetuses with RAA-RDA. Ultrasound examinations should be performed for cardiac anomalies and additional structural anomalies. Vascular ring formation is a rare but important complication due to compression risk to the trachea and esophagus.
Acknowledgments
We would like to thank the Department of Perinatology, Zeynep Kamil Teaching and Training Hospital for supporting this research.
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Research ethics: The study complies with all the relevant national regulations, institutional policies and in accordance the tenets of the Helsinki Declaration, and has been approved by the authors’ Institutional Ethics Committee.
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Informed consent: Informed consent was obtained from all individuals included in this study.
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Author contributions: All authors have accepted responsibility for the entire content of this manuscript and approved its submission.
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Competing interests: The authors state no conflicts of interest.
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Research funding: None declared.
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Data availability: The data that support the findings of this study are available from the corresponding author, upon reasonable request.
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© 2024 Walter de Gruyter GmbH, Berlin/Boston
Artikel in diesem Heft
- Frontmatter
- Opinion Paper
- The importance of professional responsibility and fetal viability in the management of abortion
- Corner of Academy
- Multifetal pregnancy reductions and selective fetocide in a tertiary referral center – a retrospective cohort study
- Original Articles – Obstetrics
- Cervical length as a screening tool for preterm birth in twin pregnancies: a systematic review and critical evaluation of quality clinical practice guidelines
- Determinants of prematurity in urban Indonesia: a meta-analysis
- Predictors of planned home birth before and during the COVID-19 pandemic
- Sensitivity of antenatal ultrasound in diagnosing posterior placenta accreta spectrum disorders
- The prognostic role of CRL discordance in first trimester ultrasound
- Evaluation of postpartum shock index in hypertensive diseases of pregnancy: a case-control study from a tertiary reference center
- Original Articles – Fetus
- Prenatal diagnosis of right aortic arch: associated anomalies and fetal prognosis according to different subtypes
- Fetal brain development in pregnancies complicated by gestational diabetes mellitus
- The association between parental SARS-CoV-2 infection in pregnancy and fetal growth restriction
- Subclinical cardiac impairments in fetuses conceived through assisted reproductive technology by speckle tracking echocardiography
- Original Articles – Neonates
- Coagulation assessment of severe acute respiratory syndrome coronavirus 2 (SARS-CoV2) infected pregnant women and their offspring by using rotational thromboelastometry (ROTEM)
- Comprehensive appraisal of pregnancy and neonatal outcomes in singleton pregnancies conceived via in vitro fertilization in the USA (2016–2021)
- Influence of donor characteristics on the milk donation volume and microbiological quality of donated human milk in first 3 years of work of the Croatian human milk bank-retrospective observational study
Artikel in diesem Heft
- Frontmatter
- Opinion Paper
- The importance of professional responsibility and fetal viability in the management of abortion
- Corner of Academy
- Multifetal pregnancy reductions and selective fetocide in a tertiary referral center – a retrospective cohort study
- Original Articles – Obstetrics
- Cervical length as a screening tool for preterm birth in twin pregnancies: a systematic review and critical evaluation of quality clinical practice guidelines
- Determinants of prematurity in urban Indonesia: a meta-analysis
- Predictors of planned home birth before and during the COVID-19 pandemic
- Sensitivity of antenatal ultrasound in diagnosing posterior placenta accreta spectrum disorders
- The prognostic role of CRL discordance in first trimester ultrasound
- Evaluation of postpartum shock index in hypertensive diseases of pregnancy: a case-control study from a tertiary reference center
- Original Articles – Fetus
- Prenatal diagnosis of right aortic arch: associated anomalies and fetal prognosis according to different subtypes
- Fetal brain development in pregnancies complicated by gestational diabetes mellitus
- The association between parental SARS-CoV-2 infection in pregnancy and fetal growth restriction
- Subclinical cardiac impairments in fetuses conceived through assisted reproductive technology by speckle tracking echocardiography
- Original Articles – Neonates
- Coagulation assessment of severe acute respiratory syndrome coronavirus 2 (SARS-CoV2) infected pregnant women and their offspring by using rotational thromboelastometry (ROTEM)
- Comprehensive appraisal of pregnancy and neonatal outcomes in singleton pregnancies conceived via in vitro fertilization in the USA (2016–2021)
- Influence of donor characteristics on the milk donation volume and microbiological quality of donated human milk in first 3 years of work of the Croatian human milk bank-retrospective observational study
