Addison’s disease presenting with perimyocarditis
-
Elisa Baranski Lamback
,
Grazia Morandi
Abstract
Background:
Polyglandular autoimmune syndrome (PGA) and eosinophilic granulomatosis with polyangiitis (EGPA) do not seem to represent a coincidental association.
Case presentation:
A case of a 15-year-old boy is reported who presented with severe systemic inflammation, perimyocarditis and cardiogenic shock, in whom EGPA was initially suspected and later diagnosed with autoimmune adrenalitis with PGA.
Conclusions:
The severity of the systemic inflammation and perimyocarditis suggests a more widespread autoimmune-mediated process. Autoimmune adrenal insufficiency should be considered in all cases of pericarditis and perimyocarditis, especially when the severity of clinical manifestations exceeds the expected for the severity of the cardiac findings, as timely identification and prompt treatment may be life-saving.
Author contributions: All the authors have accepted responsibility for the entire content of this submitted manuscript and approved submission.
Research funding: None declared.
Employment or leadership: None declared.
Honorarium: None declared.
Competing interests: The funding organization(s) played no role in the study design; in the collection, analysis, and interpretation of data; in the writing of the report; or in the decision to submit the report for publication.
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- Short-term adverse effects of testosterone used for priming in prepubertal boys before growth hormone stimulation test
- Growth response to growth hormone treatment in patients with SHOX deficiency can be predicted by the Cologne prediction model
- WHO 2006 Child Growth Standards overestimate short stature and underestimate overweight in Japanese children
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- Insulin resistance and lung function in obese asthmatic pre-pubertal children
- Obesity is associated with vitamin D deficiency in Danish children and adolescents
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Articles in the same Issue
- Frontmatter
- Editorial
- Growth and growth hormone: recent papers on efficacy and adverse effects of growth hormone and World Health Organisation growth standards
- Review
- Allergic and non-allergic skin reactions associated with growth hormone therapy: elucidation of causative agents
- Original Articles
- Adherence to growth hormone therapy in children and its potential barriers
- Short-term adverse effects of testosterone used for priming in prepubertal boys before growth hormone stimulation test
- Growth response to growth hormone treatment in patients with SHOX deficiency can be predicted by the Cologne prediction model
- WHO 2006 Child Growth Standards overestimate short stature and underestimate overweight in Japanese children
- Identifying depressive symptoms among diabetes type and the impact on hemoglobin A1c
- Insulin resistance and lung function in obese asthmatic pre-pubertal children
- Obesity is associated with vitamin D deficiency in Danish children and adolescents
- Daily sitting time associated with the risk of metabolic syndrome in Korean adolescents
- Molecular basis and clinical presentation of classic galactosemia in a Croatian population
- Clinical outcome in a series of pediatric patients with congenital generalized lipodystrophies treated with dietary therapy
- Letter to the Editor
- Spondyloepiphyseal or spondylometaphyseal dysplasia in ancient Greek art
- Case Reports
- Sirolimus therapy for congenital hyperinsulinism in an infant with a novel homozygous KCNJ11 mutation
- Veganism as a cause of iodine deficient hypothyroidism
- A case of Riley Ruvalcaba syndrome with a novel PTEN mutation accompanied by diffuse testicular microlithiasis and precocious puberty
- Addison’s disease presenting with perimyocarditis
