Complete Amino-Acid Sequence and Carbohydrate Content of the Naturally Occurring Glucosylceramide Activator Protein (A₁ Activator) Absent from a New Human Gaucher Disease Variant

Articles in the same Issue

1. Titelei
2. 7th International Symposium on Affinity Chromatography and Interfacial Macromolecular Interactions. Held in Oberammergau, August 17th — 21st, 1987
3. Electron Microscopical Investigation of Citrate Lyase Single Molecules
4. Homeothermic Fish and Hemoglobin: Primary Structure of the Hemoglobin from Bluefin Tuna (Thunnus thynnus, Scromboidei)
5. Haploid Expression of a Protamine Gene During Bovine Spermatogenesis
6. Effect of Diabetes on the Metabolism of Chenodeoxycholic Acid in Isolated Perfused Rat Liver
7. Interaction of Rat Peritoneal Macrophages with Homologous, Sialidase-Treated Lymphocytes in vitro
8. Studies on Immunoassays of Peptide Factors. II. Fluorescence Enzyme Immunoassay for Human Little-Gastrin
9. Is the Formation of AL-Type Amyloid Promoted by Structural Peculiarities of Immunoglobulin L-Chains? Primary Structure of an Amyloidogenic λ-L-Chain (BJP-ZIM)
10. Structure-Function Relationship of Mitochondrial Malate Dehydrogenase af High Dilution and in Multicomponent Systems
11. β-Lactoglobulin Identified in Marsupial Milk. The Primary Structure, Binding Site and possible Function of β-Lactoglobulin from Eastern Grey Kangaroo (Macropus giganteus)
12. Bile Acids Inhibit Secretion of Very Low Density Lipoprotein by Rat Hepatocytes
13. Formation of 4-Ethoxy-4’-nitrosodiphenylamine in the Reaction of the Phenacetin Metabolite 4-Nitrosophenetol with Glutathione
14. Phenol-Promoted Structural Transformation of Insulin in Solution
15. Studies on the Immunoglobulin V_ϰ Locus in Human Lymphoid Cell Lines
16. The N-terminal Sequence of Ribosomal Protein L10 from the Archaebacterium Halobacterium marismortui and its Relationship to Eubacterial Protein L6 and Other Ribosomal Proteins
17. 46-kDa Mannose 6-phosphate-Specific Receptor: Purification, Subunit Composition, Chemical Modification
18. 46-kDa Mannose 6-phosphate-Specific Receptor: Biosynthesis, Processing, Subcellular Location and Topology
19. The Primary Structure of the Hemoglobin of Spectacled Bear (Tremarctos ornatus, Carnivora)
20. Sex Differences in the Control of Glucose-6-phosphate Dehydrogenase and 6-Phosphogluconate Dehydrogenase. Interaction of Estrogen, Testosterone and Insulin in the Regulation of Enzyme Levels in vivo and in Cultured Hepatocytes
21. cDNA Cloning of Human Inter-α-Trypsin Inhibitor Discloses Three Different Proteins
22. Structure of the Yeast Isoleucyl-tRNA Synthetase Gene (ILS1). DNA-Sequence, Amino-Acid Sequence of Proteolytic Peptides of the Enzyme and Comparison of the Structure to those of other Known Aminoacyl-tRNA Synthetases
23. The Elastase Inhibitory Capacity and the α₁-Proteinase Inhibitor and Bronchial Inhibitor Content of Bronchoalveolar Lavage Fluids from Healthy Subjects
24. Antigen-Gelonin Conjugates. Preparation and Application in Experimental Myasthenia gravis
25. Ursprung und Geschichte der Gesellschaft für Biologische Chemie
26. Herbsttagung der Gesellschaft für Biologische Chemie. 27.—30. September 1987 in Erlangen
27. 65. Konferenz der Gesellschaft für Biologische Chemie. 1. Konferenz der Studiengruppe. Biochemische Pharmakologie und Toxikologie
28. Identification of Different Transport Systems for Bile Salts in Sinusoidal and Canalicular Membranes of Hepatocytes
29. Quantification of Kininogen in Human Renal Medulla
30. Structure and Function of L-Lactate Dehydrogenases from Thermophilic and Mesophilic Bacteria, V. The Complete Amino-Acid Sequence of the Mesophilic L-Lactate Dehydrogenase from Bacillus megaterium
31. Structure and Function of L-Lactate Dehydrogenases from Thermophilic and Mesophilic Bacteria, VI. Nucleotide Sequences of Lactate Dehydrogenase genes from the Thermophilic Bacteria Bacillus stearothermophilus, B. caldolyticus and B. caldotenax
32. Crosslinking of Phycobiliproteins from the Cyanobacterium Mastigocladus laminosus with Bis-Imidates: Localization of an Intrasubunit and an Intersubunit Crosslink in C-Phycocyanin
33. N-Terminal Amino-Acid Sequence of a Sphingolipid Activator Protein Missing in a New Human Gaucher Disease Variant
34. The Primary Structure of the Pallid Bat (Antrozous pallidus, Chiroptera) Hämoglobin
35. Hydrolysis of Human High-Molecular-Mass Kininogen by Human Plasma Kallikrein. Proposal of a New Model Concept for the Course of Reaction in Presence and Absence of C₁-Inhibitor
36. In vivo Bindung Partners of the Lens culinaris Lectin
37. Purification and Properties of a Nonheme Bromoperoxidase from Streptomyces aureofaciens
38. REVIEW
39. 63. Konferenz der Gesellschaft für Biologische Chemie. Studiengruppe Membranstrukturen und -transport. Deutsches Membranforum
40. 67. Konferenz der Gesellschaft für biologische Chemie. Biochemie des Nervensystems. Abschlußkolloquium des DFG-Schwerpunktprogramm „Biochemie des Nervensystems” gemeinsam mit der „Studiengruppe Neurochemie” der GBCh
41. The Covalent Structure of the Elastase Inhibitor from Anemonia sulcata - a “Non-Classical” Kazal-Type Protein
42. Complete Amino-Acid Sequence of Bovine Seminal Ribonuclease, a Dimeric Protein from Seminal Plasma
43. The Complete Amino-Acid Sequence of Dimeric β-Lactoglobulin from Mouflon (Ovis ammon musimon) Milk
44. Factors Limiting the Hydrolysis of Casein by Subtilisin DY
45. Structural Studies on the Murine Granulocyte Colony-Stimulating Factor
46. Neutral Proteinase Inhibitors in PMN Leukocytes. I. Purification and Characterization of a Neutral Proteinase Inhibitor from Bovine Neutrophils
47. Neutral Proteinase Inhibitors in PMN Leukocytes. II. Isolation and Characterization of a Neutral Proteinase Inhibitor from Porcine PMN Leukocytes
48. Tissue Kallikrein and Bradykinin Do Not Have Direct Insulin-like Actions on Skeletal Muscle Glucose Utilization
49. Synthesis of Human [15-Norleucine]little-gastrin-II and Des-1-tryptophan-[12-norleucine]minigastrin-II
50. High Frequency Antigens of Human Erythrocyte Membrane Sialoglycoproteins, V.Characterization of the Gerbich Blood Group Antigens: Ge2 and Ge3
51. The Primary Structure of the Hemoglobins of the Adult Jaguar (Panthera onco, Carnivora)
52. Structure and Function of L-Lactate Dehydrogenases from Thermophilic and Mesophilic Bacteria VII. Nucleotide Sequence of the Lactate Dehydrogenase Gene from the Mesophilic Bacterium Bacillus megaterium. Preparation and Properties of a Hybrid Lactate Dehydrogenase Comprising Moieties of the B. megaterium and B. stearothermophilus Enzymes
53. Isolation and Localization of N-Methylasparagine in Phycobiliproteins from the Cyanobacterium Mastigocladus laminosus
54. Interferon-γ-Induced Degradation of Tryptophan by Human Cells in vitro
55. Synthesis, Cloning and Expression of Recombinant Aprotinin
56. Inhibition of Urokinase by Protein C-Inhibitor (PCI). Evidence for Identity of PCI and Plasminogen Activator Inhibitor 3
57. Structure and Function of L-Lactate Dehydrogenase from Thermophilic, Mesophilic and Psychrophilic Bacteria, VIII. The Primary Structure of the Psychrophilic Lactate Dehydrogenase from Bacillus psychrosaccharolyticus
58. Influence of Chain Shortening on the Inhibitor Properties of Hirudin and Eglin c
59. Isolation, Characterization, and Localization of Antigen γ, a Serine Proteinase of the “Kallikrein-Family” in the Rat Submandibular Gland
60. Zinc and Cadmium 5-Aminolevulinate Dehydratase. Metal-Dependent pH Profiles
61. Reductive Alkylation of Lysine Residues in Subtilisin DY
62. Preparation and Characterization of N^ε-(2,3-Dihydroxypropyl)-L-lysine and its Phenylthiohydantoin Derivative
63. Metabolism of Ganglioside-Amides in Cultured Human Fibroblasts
64. Amino-Acid Sequences of Trypsin Inhibitors from Watermelon (Citrullus vulgaris) and Red Bryony (Bryonia dioica) Seeds
65. Prostaglandin Responses in Isolated Perfused Rat Liver: Ca^2⊕ and K^⊕ Fluxes, Hemodynamic and Metabolic Effects
66. Efficient Synthesis of N^α-Acetylarginine Methylamide
67. A Specific Enzymatic Method for the Determination of Taurine
68. Protein X, a Proteolysis Product of Human Pancreatic Juice. Immunological Relationship with Trypsinogen 1
69. Structural Relationship of an Apolipoprotein (a) Phenotype (570 kDa) to Plasminogen: Homologous Kringle Domains are Linked by Carbohydrate-Rich Regions
70. Sialinsäurehaltige Verbindungen im Hämofiltrat von Patienten mit chronischer Niereninsuffizienz, II. Isolierung und Strukturaufklärung von Sialoglycopeptiden
71. High-Altitude Respiration of Geese. The Primary Structures of the Major and Minor Hemoglobin-Components of Adult Andean Goose (Chloephaga melanoptera, Anatidae): the Mutation Leu → Ser in Position 55 of the ß-Chains
72. Complete Amino-Acid Sequence and Carbohydrate Content of the Naturally Occurring Glucosylceramide Activator Protein (A₁ Activator) Absent from a New Human Gaucher Disease Variant
73. Modulation of the Glucagon-dependent Induction of Phosphoenolpyruvate Carboxykinase by Adenosine, but not Ketone Bodies or Animonia in Rat Hepatocyte Cultures. Possible significance for the zonal heterogeneity of liver parenchyma
74. Pyroglutamyl-aprotinin, a New Aprotinin Homologue from Bovine Lungs - Isolation, Properties, Sequence Analysis and Characterization Using ¹H Nuclear Magnetic Resonance in Solution
75. Purification, some Properties of two Phospholipases A₂ (CM-I and CM-II) and the Amino-Acid Sequence of CM-II from Aspidelaps scutatus (Shield or Shield-Nose) venom
76. Trypsin-Inhibitory Activity of Ovalbumin Preparations is due to Ovomucoid
77. N^π-Methylhistidine in Myosin-Light-Chain Kinase
78. Subunit III of Bovine Procarboxypeptidase A: its Relationship to Human Pancreatic Elastase 1
79. The Major Protamine from Stallion Sperm. Isolation and Amino-acid Sequence
80. Index of Authors
81. Index of Authors