Computed tomography–guided percutaneous cryoablation of hereditary adrenal pheochromocytoma in three patients
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Emily Griffing
,
Brenton Reading
Abstract
Objectives
Pheochromocytomas (PHEO) are neuroendocrine tumors rarely diagnosed in children. We are reporting on the management challenges of three adolescent patients who present with hereditary PHEO.
Case presentation
The index patient and his male sibling presented with bilateral PHEO, while a third patient presented with a unilateral PHEO, all associated with von Hippel–Lindau (VHL) syndrome. The patients were treated with computed tomography (CT)-guided percutaneous cryoablation (CRA) of the adrenal lesions, with varying degrees of success.
Conclusions
CT-guided percutaneous CRA of hereditary PHEO has not been reported in the pediatric population and may represent a novel treatment strategy that reduces the risk of intraprocedural complications and adrenal insufficiency (AI).
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Research ethics: Not applicable.
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Informed consent: Informed consent was obtained from all individuals included in this study, or their legal guardians or wards.
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Author contributions: The authors have accepted responsibility for the entire content of this manuscript and approved its submission.
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Competing interests: The authors state no conflict of interest.
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Research funding: None declared.
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Data availability: Not applicable.
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Supplementary Material
This article contains supplementary material (https://doi.org/10.1515/jpem-2024-0033).
© 2024 Walter de Gruyter GmbH, Berlin/Boston
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Articles in the same Issue
- Frontmatter
- Editorial
- New Editor-in-Chief of the Journal of Pediatric Endocrinology and Metabolism
- Original Articles
- Mental disorders in children and adolescents with type 1 diabetes before and during the COVID-19 pandemic: results from the DPV registry
- Glucose and lipid-related indicators in relation to elevated alanine aminotransferase in a pediatric population
- Controlled attenuation parameter (CAP): the clinical value based on MRI-PDFF in children with obesity
- Presence of metabolic syndrome markers in very low birth weight ex-premature infants during early adolescence
- Benign transient hyperphosphatasemia in the pediatric population: a single center cohort study
- Growth hormone therapy does not impact the development of intracranial hypertension in children with Chiari malformation
- Evaluation of the systemic-immune inflammation index (SII) and systemic immune-inflammation response index (SIRI) in children with type 1 diabetes mellitus and its relationship with cumulative glycemic exposure
- The relationship between bisphenol A and phthalates with precocious puberty in Vietnamese children
- Case Reports
- Early juvenile cataract in newly diagnosed type 1 diabetic patients: a description of two cases
- Computed tomography–guided percutaneous cryoablation of hereditary adrenal pheochromocytoma in three patients
- Treatment modalities and outcomes in pediatric Cushing’s disease – report of three cases and literature review
- Variable presentation and outcomes of primary hyperparathyroidism in children and adolescents
