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A fatal case of congenital disseminated langerhans cell histiocytosis
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C. Goñi-Orayen
Published/Copyright:
June 1, 2005
Abstract
The case of a newborn male infant with congenital Langerhans cell histiocytosis (LCH) is presented. At birth, showed cutaneous lesions (papules and vesicles with a haemorrhagic aspect), mucosal and ganglionic involvement. Biopsy of these lesions led to the diagnosis of LCH. At 24 hours of life the patient began with respiratory, hepatic, hematological and renal dysfunction, and died at 72 hours of life, despite corticoid treatment.
LHC with vesicles and a rapid and fatal development, has previously only been described in three patients.
The differential diagnosis of a disseminated and hemorragic vesicular eruption in a newborn infant is extensive and must include LHC.
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Published Online: 2005-06-01
Published in Print: 1999-07-01
Copyright (c)1999 by Walter de Gruyter GmbH & Co. KG
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Articles in the same Issue
- The study of morphology and circulation of early embryo by three-dimensional ultrasound and power Doppler
- The merit of routine cord blood pH measurement at birth
- The influence of maternal erythrocyte deformability on fetal growth, gestational age and birthweight
- Reproductive choice in individuals HIV-1 infected in South Eastern Italy
- The sensitivity of the trivariate analysis using maternal serum alpha-feto protein, human chorionic gonadotrophin and maternal age in screening for fetal aneuploidy in mothers above the age of 35
- Neonatal and pediatric outcome of infants born to mothers with Antiphospholipid Syndrome
- Changes in cervical resistance and collagen fluorescence during gestation in rats
- The study of maternal and fetal plasma catecholamines levels during pregnancy and delivery
- Is adolescent pregnancy associated with adverse perinatal outcome?
- Physical exercise during pregnancy - physiological considerations and recommendations
- Endothelin-1 levels in infants with pulmonary hypertension receiving extracorporeal membrane oxygenation
- Maternal and neonatal outcome of twin pregnancies complicated by single fetal death
- A fatal case of congenital disseminated langerhans cell histiocytosis
- Treatment of severe postpartum hemorrhage by rectally administered gemeprost pessaries
